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CCDC103 Antibody

  • 货号：
    CSB-PA812877LA01HU
  • 规格：
    ￥440
  • 促销：
    小规格抗体限时一口价
  • 图片：
    • Western Blot
      Positive WB detected in: Mouse heart whole cell lysate
      All lanes:CCDC103 Antibody at 1:1000
      Secondary
      Goat polyclonal to rabbit IgG at 1/50000 dilution
      Predicted band size: 28kDa
      Observed band size: 28 kDa
  • 其他：

产品详情

  • 产品名称：
    Rabbit anti-Homo sapiens (Human) CCDC103 Polyclonal antibody
  • Uniprot No.：
    Q8IW40
  • 基因名：
    CCDC103
  • 别名：
    CCDC103Coiled-coil domain-containing protein 103 antibody
  • 宿主：
    Rabbit
  • 反应种属：
    Human, Mouse
  • 免疫原：
    Recombinant Human Coiled-coil domain-containing protein 103 protein (1-242AA)
  • 免疫原种属：
    Homo sapiens (Human)
  • 标记方式：
    Non-conjugated

    本页面中的产品，CCDC103 Antibody (CSB-PA812877LA01HU)，的标记方式是Non-conjugated。对于CCDC103 Antibody，我们还提供其他标记。见下表：

    可提供标记
    标记方式 货号 产品名称 应用
    HRP CSB-PA812877LB01HU CCDC103 Antibody, HRP conjugated ELISA
    FITC CSB-PA812877LC01HU CCDC103 Antibody, FITC conjugated
    Biotin CSB-PA812877LD01HU CCDC103 Antibody, Biotin conjugated ELISA
  • 克隆类型：
    Polyclonal
  • 抗体亚型：
    IgG
  • 纯化方式：
    >95%, Protein G purified
  • 浓度：
    It differs from different batches. Please contact us to confirm it.
  • 保存缓冲液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 产品提供形式：
    Liquid
  • 应用范围：
    ELISA, WB
  • 推荐稀释比：
    Application Recommended Dilution
    WB 1:1000-1:5000
  • Protocols：
  • 储存条件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 货期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.

产品评价

靶点详情

  • 功能：
    Dynein-attachment factor required for cilia motility.
  • 基因功能参考文献：
    1. The CCDC103 p.His154Pro mutation is more prevalent than previously thought in the South Asian community in the UK and causes primary ciliary dyskinesia that can be difficult to diagnose using pathology-based clinical tests. PMID: 28790179
    2. A variable and complex phenotype caused by the co-inheritance of a single gene mutation in CCDC103 and a microduplication at 17q12, both on chromosome 17. PMID: 26123568
    3. These results identify Ccdc103 as a dynein arm attachment factor that causes primary ciliary dyskinesia when mutated. PMID: 22581229
  • 相关疾病：
    Ciliary dyskinesia, primary, 17 (CILD17)
  • 亚细胞定位：
    Cytoplasm. Cell projection, cilium, flagellum.
  • 蛋白家族：
    CCDC103/PR46b family
  • 数据库链接：

    HGNC: 32700

    OMIM: 614677

    KEGG: hsa:388389

    STRING: 9606.ENSP00000387252

    UniGene: Hs.743398