ABCD1
ABCD1是一种定位于过氧化物酶体膜上的ATP结合盒式转运蛋白，具有特定的结构和功能。它利用ATP水解的能量，将超长链脂肪酸转运至过氧化物酶体进行β-氧化，维持细胞内脂质平衡。ABCD1的结构特点包括两个核苷酸结合结构域和两个跨膜结构域，这些结构域在底物结合时发生构象变化，实现底物的转运。然而，当ABCD1功能障碍时，会导致超长链脂肪酸在细胞质基质中异常积累，从而引发X-连锁肾上腺脑白质营养不良等神经退行性疾病。
热销产品
Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1)-VLPs
CSB-MP001068HU
ABCD1 Antibodies
ABCD1 for Homo sapiens (Human)
| 产品货号 | 产品名称 | 种属反应性 | 应用类型 |
|---|---|---|---|
| CSB-PA001068GA01HU | ABCD1 Antibody | Human,Mouse,Rat | ELISA,WB,IHC |
| CSB-PA214656 | ABCD1 Antibody | Human | ELISA,WB |
| CSB-PA008163 | ABCD1 Antibody | Human | WB, ELISA |
| CSB-PA001068LA01HU | ABCD1 Antibody | Human | ELISA, IHC |
ABCD1 Proteins
ABCD1 Proteins for Homo sapiens (Human)
| 产品货号 | 产品名称 | 来源 |
|---|---|---|
| CSB-YP001068HU1 CSB-EP001068HU1 CSB-BP001068HU1 CSB-MP001068HU1 CSB-EP001068HU1-B |
Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
| CSB-CF001068HU | Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1) (Active) | in vitro E.coli expression system |
| CSB-MP001068HU | Recombinant Human ATP-binding cassette sub-family D member 1 (ABCD1)-VLPs | Mammalian cell |
